The Enigmatic Autoimmune Response in Endemic Pemphigus Foliaceus
نویسندگان
چکیده
منابع مشابه
The enigmatic autoimmune response in endemic pemphigus foliaceus.
Endemic pemphigus foliaceus, known as Fogo Selvagem (FS) in Brazil, is a disease characterized by subcorneal blisters and IgG4 anti-dermoglein 1 (Dsg1) autoantibodies. Epidemiological studies of FS strongly an environmental etiology. A 15-year surveillance of the Limao Verde Amerindian reservation in Brazil has uncovered information on the transition of the autoimmune response from the pre-clin...
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The word “pemphigus” is derived from the Greek term "pemphix” meaning bubble or blister. Pemphigus is a group of autoimmune diseases (see Table 4) characterized by intra-epithelial blistering, resulting in superficial vesicles or bullae that easily rupture, resulting in ulceration of mucosal and/or cutaneous sites. Although rare, pemphigus causes significant morbidity and potential mortality fo...
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ژورنال
عنوان ژورنال: Actas Dermo-Sifiliográficas
سال: 2009
ISSN: 0001-7310
DOI: 10.1016/s0001-7310(09)73377-0